Persistent hyperplastic primary vitreous

Persistent hyperplastic primary vitreous
Classification and external resources

Falciform fold of detached dysplastic retina encircles the persistent hyaloid artery that extends from the optic nerve head to the retrolental mass.
ICD-10 GroupMajor.minor
ICD-9 xxx

Persistent hyperplastic primary vitreous (PHPV) is a rare congenital developmental anomaly of the eye that results following failure of the embryological, primary vitreous and hyaloid vasculature to regress[1]. It can be present in three forms: purely anterior (persistent tunica vasculosa lentis and persistent posterior fetal fibrovascular sheath of the lens), purely posterior (falciform retinal septum and ablatio falcicormis congentia) and a combination of both[1].

Contents

Causes/association of bilateral PHPV

1. Trisomy 13 (Patau's syndrome) 2. Norries disease 3. Walker Warburg syndrome

Symptoms

The primary vitreous used in formation of the eye during fetal development remains in the eye upon birth and is hazy and scarred.[2]

See also

References

  1. ^ a b Silbert, Mira; Gunvood, Andrew S. (2000). "Clinical review, Persistent hyperplastic primary vitreous". Clinical Eye and Vision Care (Ireland: Elsevier Science Ireland Ltd.) 12 (3-4): 131–137. doi:10.1016/S0953-4431(00)00054-0. PMID 11137427. http://www.sciencedirect.com/science?_ob=ArticleURL&_udi=B6T5B-41Y8720-6&_user=1069331&_rdoc=1&_fmt=&_orig=search&_sort=d&view=c&_acct=C000051277&_version=1&_urlVersion=0&_userid=1069331&md5=fe05817e301fbf187cac5d8aaa1178ac. Retrieved 2009-05-11. 
  2. ^ Young, Jane. "Persistent Hyperplastic Primary Vitreous". http://www.fevr.net/About%20FEVR/persistent_hyperplastic_primary.htm. Retrieved 2009-05-11. 

External links